Syringocystadenoma papilliferum

Orpha code: 840OMIM code:

Definition

A rare non-malignant adnexal neoplasm that originates from the apocrine or eccrine sweat glands and is characterized histologically by cystic, papillary, and ductal invaginations into the dermis lined by double-layered outer cuboidal and luminal high columnar epithelium and connected to the epidermis. Dilated capillaries and a dense infiltrate of plasma cells are characteristic. Clinically, lesions are asymptomatic with a heterogeneous, non-distinctive appearance ranging from skin-colored to pink papules or plaques, occurring most commonly in the head and neck area.

Disease data
Classification

Disease

Synonyms
Fistulous vegetative verrucous hydradenoma
SCAP
Torbielakogruczolak brodawkujący
Naevus syringocystadenomatosus papilliferus
Papillary syringocystadenoma
SCAP
Syringadenoma papilliferum
ORPHA code
840
OMIM code
-
ICD10 code
D23.9
ICD11 code
LC0Y

No additional description.

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