Desmoplastic small round cell tumor

Orpha code: 83469OMIM code:

Definition

An aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases.

Disease data
Classification

Disease

Synonyms
DSRCT
DSRCT
ORPHA code
83469
OMIM code
-
ICD10 code
C48.2
ICD11 code
-

No additional description.

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