Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare multisystemic, autoinflammatory disorder of unknown etiology characterized by the formation of immune, non-caseating granulomas in any organ(s), leading to variable clinical symptoms and severity. Clinical presentation is typically with persistent dry cough, eye or skin manifestations, peripheral lymph nodes, fatigue, weight loss, fever or night sweats, and Löfgren syndrome. Disease data Klasyfikacja Disease Synonimy Besnier-Boeck-Schaumann disease Choroba Besniera, Boecka i Schaumanna Boeck sarcoid Kod ORPHA 797 Kod OMIM 612388 Kod ICD10 D86.8 Kod ICD11 4B20 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl