Microcystic lymphatic malformation

Orpha code: 79490OMIM code:

Definition

A rare common cystic lymphatic malformation characterized by a benign cystic lesion composed of dilated lymphatic channels. Microcystic lesions consist of cysts smaller than 1 cm in diameter. They usually present at birth or during the first years of life and most often occur in the head and neck region but may affect any site. Symptoms depend on the location and extent of the lesion. Infection, trauma, or intracystic hemorrhage can lead to lesional expansion. Malignant transformation does not occur.

Disease data
Classification

Malformation syndrome

Synonyms
Capillary lymphangioma
Malformacja limfatyczna kapilarna
Malformacja limfatyczna powierzchowna
Naczyniak limfatyczny kapilarny
Naczyniak limfatyczny mikrotorbielowaty
Naczyniak limfatyczny powierzchowny
Capillary lymphatic malformation
Cutaneous lymphangioma circumscriptum
Microcystic infiltrating lymphatic malformation
Microcystic lymphangioma
Superficial lymphangioma
Superficial lymphatic malformation
ORPHA code
79490
OMIM code
-
ICD10 code
D18.1
ICD11 code
LA90.11

No additional description.

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