Macrocystic lymphatic malformation

Orpha code: 79489OMIM code:

Definition

A rare common cystic lymphatic malformation characterized by a benign cystic lesion composed of dilated lymphatic channels. Macrocystic lesions consist of cysts larger than 1 cm in diameter. They usually present at birth or during the first years of life and most often occur in the head and neck region but may affect any site. Symptoms depend on the location and extent of the lesion. Infection, trauma, or intracystic hemorrhage can lead to lesional expansion. Malignant transformation does not occur.

Disease data
Classification

Malformation syndrome

Synonyms
Cavernous lymphangioma
Jamista malformacja limfatyczna
Macrocystic lymphangioma
Naczyniak limfatyczny jamisty
Cavernous lymphatic malformation
Macrocystic lymphangioma
ORPHA code
79489
OMIM code
-
ICD10 code
D18.1
ICD11 code
LA90.10

No additional description.

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