3-phosphoglycerate dehydrogenase deficiency, infantile/juvenile form

Orpha code: 79351OMIM code: 601815

Definicja

3-Phosphoglycerate dehydrogenase deficiency (3-PGDH deficiency) is an autosomal recessive form of serine deficiency syndrome (see this term) characterized clinically in the few reported cases by congenital microcephaly, psychomotor retardation and intractable seizures in the infantile form and by absence seizures, moderate developmental delay and behavioral disorders in the juvenile form

Disease data
Klasyfikacja

Etiological subtype

Synonimy
PHGDH deficiency, infantile/juvenile form
PHGDH deficiency, infantile/juvenile form
Kod ORPHA
79351
Kod OMIM
601815
Kod ICD10
E72.8
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl