Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A form of congenital diazoxide-resistant hyperinsulinism characterized by recurrent episodes of profound hypoglycemia caused by an excessive/uncontrolled insulin secretion (inappropriate for the level of glycemia) due to a focal adenomatous hyperplasia of pancreas, that is unresponsive to medical treatment with diazoxide. Disease data Classification Clinical group Synonyms Hyperinsulinemic hypoglycemia, diazoxide-resistant focal form Hipoglikemia hiperinsulinemiczna, forma ogniskowa oporna na diazoksyd ORPHA code 79298 OMIM code - ICD10 code E16.1 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl