Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Familial progressive hyperpigmentation is a rare, genetic, skin pigmentation anomaly disorder characterized by irregular patches of hyperpigmented skin which present at birth or in early infancy and increase in size, number and confluence with age. Affected areas of the body include the face, neck, trunk and limbs, as well as the palms, soles, oral mucosa and conjuctiva. No hypogmentation macules are observed and no systemic diseases are associated. Disease data Classification Disease Synonyms Melanosis diffusa congenita Dziedziczna melanoza uogólniona Universal melanosis Wrodzona melanoza rozsiana Melanosis universalis hereditaria Universal melanosis ORPHA code 79146 OMIM code 614233 ICD10 code L81.4 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl