Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja Familial progressive hyperpigmentation is a rare, genetic, skin pigmentation anomaly disorder characterized by irregular patches of hyperpigmented skin which present at birth or in early infancy and increase in size, number and confluence with age. Affected areas of the body include the face, neck, trunk and limbs, as well as the palms, soles, oral mucosa and conjuctiva. No hypogmentation macules are observed and no systemic diseases are associated. Disease data Klasyfikacja Disease Synonimy Melanosis diffusa congenita Dziedziczna melanoza uogólniona Universal melanosis Wrodzona melanoza rozsiana Melanosis universalis hereditaria Universal melanosis Kod ORPHA 79146 Kod OMIM 614233 Kod ICD10 L81.4 Kod ICD11 - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl