Lymphoid interstitial pneumonia

Orpha code: 79128OMIM code: 247610

Definition

A rare idiopathic interstitial pneumonia characterized by a diffuse, dense, polyclonal lymphoid cell infiltration of the pulmonary interstitium and air spaces, with high prevalence in patients with immune dysregulation. Presenting symptoms are non-specific and include dyspnea and cough. The clinical course is highly variable, ranging from spontaneous resolution to progressive, fatal respiratory failure.

Disease data
Classification

Disease

Synonyms
Lymphocytic interstitial pneumonia
Limfocytarne śródmiąższowe zapalenie płuc
ORPHA code
79128
OMIM code
247610
ICD10 code
J84.1
ICD11 code
CB03.5

No additional description.

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