Lymphoid interstitial pneumonia

Orpha code: 79128OMIM code: 247610

Definicja

A rare idiopathic interstitial pneumonia characterized by a diffuse, dense, polyclonal lymphoid cell infiltration of the pulmonary interstitium and air spaces, with high prevalence in patients with immune dysregulation. Presenting symptoms are non-specific and include dyspnea and cough. The clinical course is highly variable, ranging from spontaneous resolution to progressive, fatal respiratory failure.

Disease data
Klasyfikacja

Disease

Synonimy
Lymphocytic interstitial pneumonia
Limfocytarne śródmiąższowe zapalenie płuc
Kod ORPHA
79128
Kod OMIM
247610
Kod ICD10
J84.1
Kod ICD11
CB03.5

No additional description.

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