Interstitial granulomatous dermatitis with arthritis

Orpha code: 79099OMIM code:

Definition

Interstitial granulomatous dermatitis with arthritis is a rare rheumatologic disease characterized by the occurrence of inflammatory arthritis in association with large, erythematous, symmetrical cutaneous lesions (ranging from typical, but infrequent, cord-like lesions on the flanks to more common violaceous plaques on the trunk and limbs) featuring a typical histologic infiltrate mainly constituted of histiocytes.

Disease data
Classification

Disease

Synonyms
Ackerman dermatitis syndrome
IGDA
Zespół zapalenia skóry Ackermana
Ackerman syndrome
IGDA
ORPHA code
79099
OMIM code
-
ICD10 code
D89.8
ICD11 code
-

No additional description.

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