Primary lymphedema

Orpha code: 77240OMIM code:

Definition

Primary lymphedema is a lymphatic system malformation characterized by swelling of an extremity that can be associated with other lymphatic effusions, due to an underlying developmental anomaly of the lymphatic system (abnormal lymphoangiogenesis). It can be hereditary or not and be congenital or late onset.

Disease data
Classification

Category

Synonyms
Troncular lymphatic malformation
ORPHA code
77240
OMIM code
-
ICD10 code
I89.0
ICD11 code
BD93.0

No additional description.

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