Androgen insensitivity syndrome

Orpha code: 754OMIM code:

Definition

A disorder of sex development (DSD) characterized by the presence of female external genitalia, ambiguous genitalia or variable defects in virilization in a 46,XY individual with absent or partial responsiveness to age-appropriate levels of androgens. It comprises two clinical subgroups: complete AIS (CAIS) and partial AIS (PAIS).

Disease data
Classification

Clinical group

Synonyms
AIS
AIS
Zespół feminizujących jąder
Zespół Goldberga i Maxwella
Zespół Morrisa
Zespół oporności na androgeny
Androgen resistance syndrome
Goldberg-Maxwell syndrome
Morris syndrome
Testicular feminization syndrome
ORPHA code
754
OMIM code
-
ICD10 code
E34.5
ICD11 code
LD2A.4

No additional description.

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