Renal nutcracker syndrome

Orpha code: 71273OMIM code:

Definition

A rare, syndromic renal disease characterized by the entrapment of left renal vein (LRV) between the superior mesenteric artery (SMA) and the abdominal aorta, resulting in increased luminal pressure, renal hilar varices, hematuria and, at the microscopic level, rupture of thin-walled veins into the collecting system in renal fornices.

Disease data
Classification

Disease

Synonyms
Left renal vein entrapment syndrome
RNS
Zespół uwięźnięcia lewej żyły nerkowej
RNS
ORPHA code
71273
OMIM code
-
ICD10 code
Q64.8
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl