Pemphigus vulgaris

Definition

A rare autoimmune bullous skin diseases characterized by painful, flaccid blisters and erosions of the oral mucosa, predominantly involving the buccal area, and with or without extension to the epidermis. Mucosa of the larynx, oesophagus, conjunctiva, nose, genitalia and anus, are less frequently affected.

Disease data

Classification

Disease

ORPHA code

704

OMIM code

169610

ICD10 code

L10.0

ICD11 code

EB40.0

*Soruce