Pelizaeus-Merzbacher disease

Orpha code: 702OMIM code: 213900

Definition

Pelizaeus-Merzbacher disease (PMD) is an X-linked leukodystrophy characterized by developmental delay, nystagmus, hypotonia, spasticity, and variable intellectual deficit. It is classified into three sub-forms based on the age of onset and severity: connatal, transitional, and classic PMD (see these terms).

Disease data
Classification

Disease

Synonyms
Diffuse familial brain sclerosis
PMD
PMD
Pelizaeus-Merzbacher brain sclerosis
Sudanophilic leukodystrophy, Paelizeus-Merzbacher type
ORPHA code
702
OMIM code
213900
ICD10 code
E75.2
ICD11 code
8A44.0

No additional description.

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