Malignant atrophic papulosis

Orpha code: 679OMIM code: 602248

Definition

Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal.

Disease data
Classification

Disease

Synonyms
Degos disease
Choroba Degosa
Choroba Köhlmeiera i Degosa
Grudkowatość złośliwa zanikowa
Zespół Köhlmeiera, Degosa, Delorta i Tricorta
Köhlmeier-Degos disease
Köhlmeier-Degos-Delort-Tricort syndrome
Papulosis atrophican maligna
ORPHA code
679
OMIM code
602248
ICD10 code
I77.8
ICD11 code
EF5Y

No additional description.

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