Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Malignant atrophic papulosis (MAP) is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Systemic lesions may affect the gastrointestinal tract and the central nervous system (CNS) and are potentially lethal. Disease data Classification Disease Synonyms Degos disease Choroba Degosa Choroba Köhlmeiera i Degosa Grudkowatość złośliwa zanikowa Zespół Köhlmeiera, Degosa, Delorta i Tricorta Köhlmeier-Degos disease Köhlmeier-Degos-Delort-Tricort syndrome Papulosis atrophican maligna ORPHA code 679 OMIM code 602248 ICD10 code I77.8 ICD11 code EF5Y *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl