Hereditary chronic pancreatitis

Orpha code: 676OMIM code: 167800

Definition

A rare gastroenterologic disease characterized by recurrent acute pancreatitis and/or chronic pancreatitis in at least 2 first-degree relatives, or 3 or more second-degree relatives in 2 or more generations, for which no predisposing factors are identified. This rare inherited form of pancreatitis leads to irreversible damage to both exocrine and endocrine components of the pancreas.

Disease data
Classification

Disease

ORPHA code
676
OMIM code
167800
ICD10 code
K86.1
ICD11 code
DC32.2

No additional description.

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