Extracutaneous mastocytoma

Definition

A rare neoplastic disease characterized by a localized, unifocal, low-grade tumor composed of mature mast cells, without evidence of systemic mastocytosis or skin lesions. The tumor most commonly arises in the lung and shows a non-destructive growth pattern.

Disease data

Classification

Disease

ORPHA code

66662

OMIM code

ICD10 code

C96.2

ICD11 code

2A21.3

*Soruce