Multiple endocrine neoplasia type 1

Orpha code: 652OMIM code: 131100

Definition

A rare inherited cancer syndrome, characterized by the development of multiple neuroendocrine tumors of the parathyroids, gastro-entero-pancreatic tract, and anterior pituitary gland, and less commonly the adrenal cortical gland, thymus and bronchi, with other non-endocrine tumors in some patients.

Disease data
Classification

Disease

Synonyms
MEN1
MEN 1
Zespół Wermera
Wermer syndrome
ORPHA code
652
OMIM code
131100
ICD10 code
D44.8
ICD11 code
2F7A.0

No additional description.

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