Pulmonary blastoma

Orpha code: 64741OMIM code:

Definition

A biphasic primary lung neoplasm, belonging to the group of sarcomatoid lung carcinomas (SLCs). The tumor contains both an epithelial well-differentiated component, showing tubular architecture resembling the normal fetal lung, and a mesenchymal undifferentiated stroma with a so-called ''blastema-like'' configuration that resembles an embryonic lung.

Disease data
Classification

Disease

Synonyms
Pneumoblastoma
Pneumoblastoma
ORPHA code
64741
OMIM code
-
ICD10 code
C34.3
ICD11 code
-

No additional description.

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