Medulloblastoma

Definition

A rare embryonic tumor of the neuroepithelial tissue characterized clinically by increased intracranial pressure and cerebellar dysfunction, with the most common presenting symptoms being headache, vomiting, and ataxia. The disease can be classified according to histological (classic, anaplastic, large-cell, or desmoplatic medulloblastoma, or medulloblastoma with extensive nodularity) and molecular criteria (WNT-activated, sonic-hedgehog-activated, group 3, group 4).

Disease data

Classification

Disease

ORPHA code

616

OMIM code

155255

ICD10 code

C71.6

ICD11 code

2A00.10

*Soruce