Mucolipidosis type III

Orpha code: 577OMIM code: 252605

Definition

A rare lysosomal disease characterized by dysmorphic features and skeletal changes, restricted joint mobility, short stature, and hand deformities (such as claw hands, stiffness of hands, carpal tunnel syndrome, inability to make fists). Most patients have normal intellectual capacity and the clinical progression is less rapid than that of mucolipidosis type II (MLII).

Disease data
Classification

Disease

Synonyms
Pseudo-Hurler polydystrophy
Polidystrofia pseudo-Hurler
ORPHA code
577
OMIM code
252605
ICD10 code
E77.0
ICD11 code
5C56.20

No additional description.

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