Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Muckle-Wells syndrome (MWS) is an intermediate form of cryopyrin-associated periodic syndrome (CAPS; see this term) and is characterized by recurrent fever (with malaise and chills), recurrent urticaria-like skin rash, sensorineural deafness, general signs of inflammation (eye redness, headaches, arthralgia/myalgia) and potentially life-threatening secondary amyloidosis (AA type). Disease data Classification Disease Synonyms Neutrophilic urticaria Pokrzywka neutrofilowa ORPHA code 575 OMIM code 191900 ICD10 code E85.0 ICD11 code 4A60.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl