Parenteral nutrition-associated cholestasis

Orpha code: 567983OMIM code:

Definicja

A rare hepatic disease characterized by intrahepatic cholestasis and deterioration of liver function in patients receiving parenteral nutrition for extended periods of time (signs may appear as early as within the first two weeks of initiation of parenteral nutrition). The condition commonly occurs in neonates and usually resolves with transition to enteral feeding, although severe cases may progress to liver fibrosis, cirrhosis, and portal hypertension.

Disease data
Klasyfikacja

Particular clinical situation in a disease or syndrome

Synonimy
PNAC
PNAC
Kod ORPHA
567983
Kod OMIM
-
Kod ICD10
K76.8
Kod ICD11
DB99.60

No additional description.

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