Parenteral nutrition-associated cholestasis

Orpha code: 567983OMIM code:

Definition

A rare hepatic disease characterized by intrahepatic cholestasis and deterioration of liver function in patients receiving parenteral nutrition for extended periods of time (signs may appear as early as within the first two weeks of initiation of parenteral nutrition). The condition commonly occurs in neonates and usually resolves with transition to enteral feeding, although severe cases may progress to liver fibrosis, cirrhosis, and portal hypertension.

Disease data
Classification

Particular clinical situation in a disease or syndrome

Synonyms
PNAC
PNAC
ORPHA code
567983
OMIM code
-
ICD10 code
K76.8
ICD11 code
DB99.60

No additional description.

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