Idiopathic steroid-resistant nephrotic syndrome

Orpha code: 567548OMIM code: 619263

Definicja

A rare, idiopathic nephrotic syndrome characterized by the triad of proteinuria, hypoalbuminemia and edema in patients who do not respond, or only partially respond, to the initial trial of corticosteroids. Patients may be multidrug resistant or may be sensitive to second-line immunosuppressive therapy.

Disease data
Klasyfikacja

Clinical syndrome

Synonimy
Idiopathic SRNS
Idiopathic SRNS
Kod ORPHA
567548
Kod OMIM
619263
Kod ICD10
N04.8
Kod ICD11
-

No additional description.

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