Idiopathic steroid-resistant nephrotic syndrome

Orpha code: 567548OMIM code: 619263

Definition

A rare, idiopathic nephrotic syndrome characterized by the triad of proteinuria, hypoalbuminemia and edema in patients who do not respond, or only partially respond, to the initial trial of corticosteroids. Patients may be multidrug resistant or may be sensitive to second-line immunosuppressive therapy.

Disease data
Classification

Clinical syndrome

Synonyms
Idiopathic SRNS
Idiopathic SRNS
ORPHA code
567548
OMIM code
619263
ICD10 code
N04.8
ICD11 code
-

No additional description.

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