Idiopathic non-lupus full-house nephropathy

Orpha code: 567544OMIM code:

Definition

A rare idiopathic glomerular clinical syndrome characterized by diffuse renal lesions that are indistinguishable from the lesions observed in systemic lupus erythematosus (SLE) in the absence of circulating autoantibodies and other systemic features necessary to meet the classification criteria for SLE. Patients may present with nephrotic syndrome, abnormal urinary sediment, acute renal insufficiency, progressive glomerulonephritis, and hypertension. Some patients have been reported to develop a progression to SLE over time.

Disease data
Classification

Clinical syndrome

Synonyms
Idiopathic non-lupus FHN
Idiopathic non-lupus FHN
ORPHA code
567544
OMIM code
-
ICD10 code
N05
ICD11 code
-

No additional description.

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