Idiopathic non-lupus full-house nephropathy

Orpha code: 567544OMIM code:

Definicja

A rare idiopathic glomerular clinical syndrome characterized by diffuse renal lesions that are indistinguishable from the lesions observed in systemic lupus erythematosus (SLE) in the absence of circulating autoantibodies and other systemic features necessary to meet the classification criteria for SLE. Patients may present with nephrotic syndrome, abnormal urinary sediment, acute renal insufficiency, progressive glomerulonephritis, and hypertension. Some patients have been reported to develop a progression to SLE over time.

Disease data
Klasyfikacja

Clinical syndrome

Synonimy
Idiopathic non-lupus FHN
Idiopathic non-lupus FHN
Kod ORPHA
567544
Kod OMIM
-
Kod ICD10
N05
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl