Adamantinoma

Orpha code: 55881OMIM code: 102660

Definition

A rare, primary low-grade malignant bone tumor that occurs in more than 80% of cases on the anterior surface of the tibia (tibial dyaphysis). Most cases are symptomatic or present with pain, swelling, bowing deformity or pathological fracture. Metastases especially in the lungs may be observed.

Disease data
Classification

Disease

Synonyms
Adamantinoma of long bones
Adamantinoma of long bones
ORPHA code
55881
OMIM code
102660
ICD10 code
C40.2
ICD11 code
XH8F52

No additional description.

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