Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A subtype of inflammatory pseudotumor of the liver characterized by a benign, well-circumscribed tumor with diffuse lymphoplasmacytic infiltration with histological features of IgG4-related disease (numerous IgG4-positive plasma cells, prominent eosinophils, stromal fibrosis, fibroblastic proliferations and, frequently, obliterative phlebitis), and that is likely located around the hepatic hilum. Most often it is discovered as an incidental finding. Disease data Classification Clinical subtype Synonyms IgG4-related inflammatory pseudotumor of the liver Guz rzekomy limfoplazmatyczny zapalny wątroby związany z IgG4 ORPHA code 555437 OMIM code - ICD10 code K75.8 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl