Thrombotic thrombocytopenic purpura

Orpha code: 54057OMIM code: 274150

Definition

An aggressive and life-threatening form of thrombotic microangiopathy (TMA) characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and organ failure of variable severity and is comprised of a congenital (cTTP) and acquired, immune-mediated (iTTP) form.

Disease data
Classification

Disease

Synonyms
Moschcowitz disease
Choroba Moschcowitza
TTP
TTP
ORPHA code
54057
OMIM code
274150
ICD10 code
M31.1
ICD11 code
3B64.14

No additional description.

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