Bullous pyoderma gangrenosum

Orpha code: 538869OMIM code:

Definicja

A rare subtype of pyoderma gangrenosum disease characterized by grouped vesicles that rapidly spread and coalesce to form large bullae, which evolve into ulcerations that have an erythematous peripheral halo and central necrosis, mainly affecting the upper limbs and face. Lymphoproliferative diseases are frequently associated, thus prognosis is often compromised.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Phemphigoid pyoderma gangrenosum
Phemphigoid pyoderma gangrenosum
Kod ORPHA
538869
Kod OMIM
-
Kod ICD10
L88
Kod ICD11
-

No additional description.

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