Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare subtype of pyoderma gangrenosum disease characterized by grouped vesicles that rapidly spread and coalesce to form large bullae, which evolve into ulcerations that have an erythematous peripheral halo and central necrosis, mainly affecting the upper limbs and face. Lymphoproliferative diseases are frequently associated, thus prognosis is often compromised. Disease data Classification Clinical subtype Synonyms Phemphigoid pyoderma gangrenosum Phemphigoid pyoderma gangrenosum ORPHA code 538869 OMIM code - ICD10 code L88 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl