Pustular pyoderma gangrenosum

Definition

A rare subtype of pyoderma gangrenosum characterized by multiple painful, sterile pustules with a surrounding erythematous halo, predominantly occurring on the trunk and extensor surfaces of the limbs, and potentially persisting for months. Histopathology shows a dermal neutrophilic infiltrate and subcorneal neutrophilic micropustules. The condition is commonly associated with inflammatory bowel disease.

Disease data

Classification

Clinical subtype

ORPHA code

538866

OMIM code

ICD10 code

L88

ICD11 code

*Soruce