Neurodevelopmental delay-seizures-ophthalmic anomalies-osteopenia-cerebellar atrophy syndrome

Orpha code: 529665OMIM code: 617810

Definicja

A rare, genetic, syndromic intellectual disability characterized by global developmental delay, early-onset seizures, cerebellar atrophy, osteopenia, nystagmus and dysmorphic facial features, including bitemporal narrowing, prominent forehead, anteverted nares. Dysarthria, dysmetria, ataxic gait, spasticity and dysmorphic features have also been associated.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
GPAA1-related biosynthesis defect
GPAA1-related biosynthesis defect
Kod ORPHA
529665
Kod OMIM
617810
Kod ICD10
-
Kod ICD11
-

No additional description.

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