Mirizzi syndrome

Definition

A rare biliary tract disease characterized by external compression and subsequent obstruction of an extrahepatic biliary duct by one or more gallstones in the cystic duct or the gallbladder. Patients may present with acute or chronic cholecystitis with right upper abdominal pain, nausea, and vomiting, jaundice, or cholangitis. Cholecystobiliary or -enteric fistulae can arise due to chronic inflammation and ulceration.

Disease data

Classification

Clinical syndrome

Synonyms

Extrinsic biliary compression syndrome

ORPHA code

521219

OMIM code

ICD10 code

K80.8

ICD11 code

*Soruce