Isolated microspherophakia

Definition

A rare disorder of the anterior segment of the eye characterized by the presence of an unusually small and spherical lens with increased anteroposterior thickness, and visibility of the lens equator on full mydriasis. The condition is typically bilateral and may be associated with lens dislocation or subluxation, lenticular myopia, and secondary angle-closure glaucoma.

Disease data

Classification

Morphological anomaly

ORPHA code

519396

OMIM code

ICD10 code

Q12.4

ICD11 code

LA12.3

*Soruce