Vulvar adenocarcinoma

Orpha code: 494454OMIM code:

Definition

A rare vulvar carcinoma characterized by a malignant epithelial neoplasm of glandular origin and/or with glandular characteristics arising in the vulva, including adenocarcinoma of mammary gland type, sweat gland type, and intestinal type, as well as adenocarcinomas of the Bartholin glands and Paget disease of the vulva. Depending on the type of tumor and disease stage, patients may present with a solitary vulvar mass, bleeding, or (in the case of Paget disease) a pruritic, erythematous, eczematous lesion.

Disease data
Classification

Histopathological subtype

Synonyms
Adenocarcinoma of the vulva
Gruczolak złośliwy sromu
ORPHA code
494454
OMIM code
-
ICD10 code
C51.8
ICD11 code
-

No additional description.

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