Idiopathic peliosis hepatis

Orpha code: 480524OMIM code:

Definicja

A rare vascular liver disease characterized by widespread or focal cystic dilatation of sinusoidal blood-filled spaces of the liver without any known cause. Lesions can vary in diameter between few millimeters and several centimeters. The condition may remain asymptomatic or manifest with complications including rupture and intraperitoneal hemorrhage, hepatomegaly, portal hypertension, cholestasis, and liver failure.

Disease data
Klasyfikacja

Disease

Synonimy
Idiopathic peliosis hepatitis
Idiopathic peliosis hepatitis
Kod ORPHA
480524
Kod OMIM
-
Kod ICD10
-
Kod ICD11
-

No additional description.

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