Paroxysmal extreme pain disorder

Orpha code: 46348OMIM code: 167400

Definition

A rare, genetic, neurological disorder characterized by severe episodic perirectal pain accompanied by skin flushing that is typically precipitated by defecation. Ocular and submaxillary pain, associated with triggers including cold or other irritants, may become more prominent with age.

Disease data
Classification

Disease

Synonyms
Familial rectal pain
Rodzinny ból odbytnicy
ORPHA code
46348
OMIM code
167400
ICD10 code
G90.8
ICD11 code
-

No additional description.

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