Paroxysmal extreme pain disorder

Orpha code: 46348OMIM code: 167400

Definicja

A rare, genetic, neurological disorder characterized by severe episodic perirectal pain accompanied by skin flushing that is typically precipitated by defecation. Ocular and submaxillary pain, associated with triggers including cold or other irritants, may become more prominent with age.

Disease data
Klasyfikacja

Disease

Synonimy
Familial rectal pain
Rodzinny ból odbytnicy
Kod ORPHA
46348
Kod OMIM
167400
Kod ICD10
G90.8
Kod ICD11
-

No additional description.

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