Retiform hemangioendothelioma

Orpha code: 458763OMIM code:

Definition

A rare vascular tumor characterized by a slowly growing lesion with predominant involvement of the skin and subcutaneous tissue of the distal extremities. Distinctive arborizing blood vessels lined by endothelial cells with characteristic hobnail morphology are a typical feature. Local recurrences are frequent unless wide local excision is performed, while metastasis is rare.

Disease data
Classification

Disease

ORPHA code
458763
OMIM code
-
ICD10 code
D48.1
ICD11 code
-

No additional description.

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