Intellectual disability-muscle weakness-short stature-facial dysmorphism syndrome

Orpha code: 457365OMIM code:

Definition

A rare genetic multiple congenital anomalies/dysmorphic syndrome characterized by intellectual disability, developmental delay, delayed bone age, short stature, generalized muscle weakness, and dysmorphic facial features (such as high arched eyebrows, downslanting palpebral fissures, prominent nose, and narrow palate and mouth). Additional reported manifestations include blue sclerae, ophthalmoplegia, and intention tremor. Brain imaging may show white matter abnormalities.

Disease data
Classification

Malformation syndrome

ORPHA code
457365
OMIM code
-
ICD10 code
-
ICD11 code
-

No additional description.

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