Microcephaly-corpus callosum hypoplasia-intellectual disability-facial dysmorphism syndrome

Orpha code: 457284OMIM code: 616362

Definition

A rare genetic multiple congenital anomalies/dysmorphic syndrome characterized by variable degrees of developmental delay and intellectual disability with poor or absent speech, hypotonia, hypoplastic or absent corpus callosum, and facial dysmorphism (such as long face, frontal bossing, hypertelorism, downslanting palpebral fissures, and tented upper lip). Additional reported features include microcephaly, seizures, gait ataxia, scoliosis, and syndactyly of fingers, among others.

Disease data
Classification

Malformation syndrome

ORPHA code
457284
OMIM code
616362
ICD10 code
-
ICD11 code
-

No additional description.

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