Anti-p200 pemphigoid

Definition

A rare, acquired, subepidermal autoimmune bullous disease characterized by polymorphic cutaneous lesions (blisters, urticarial lesions or scars/milia) associated with imunoglubulin G deposition in the basement membrane zone. Lesions are frequently localized on extremities, trunk, palmoplantar and cephalic areas as well as mucous membranes.

Disease data

Classification

Disease

ORPHA code

454710

OMIM code

ICD10 code

L12.8

ICD11 code

*Soruce