Primary cutaneous plasmacytosis

Orpha code: 451602OMIM code:

Definition

A rare acquired skin disease characterized by benign proliferation of mature plasma cells with a typical triad of cutaneous lesions, polyclonal hypergammaglobulinemia, and superficial lymphadenopathy, without an apparent underlying cause. The skin lesions consist of multiple round-to-oval, red-to-dark-brown macules, papules, and plaques most commonly found on the trunk, but also the face, neck, and axillae.

Disease data
Classification

Disease

ORPHA code
451602
OMIM code
-
ICD10 code
L98.6
ICD11 code
-

No additional description.

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