Autosomal recessive spastic paraplegia type 9B

Orpha code: 447760OMIM code: 616586

Definition

A rare complex hereditary spastic paraplegia characterized by early onset of slowly progressive spastic para- or tetraparesis, increased tendon reflexes, positive Babinski sign, global developmental delay, cognitive impairment, and pseudobulbar palsy. Additional manifestations include dysmorphic facial features, tremor, short stature, and urinary incontinence.

Disease data
Classification

Disease

Synonyms
AR-SPG9B
AR-SPG9B
ORPHA code
447760
OMIM code
616586
ICD10 code
G11.4
ICD11 code
-

No additional description.

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