Combined oxidative phosphorylation defect type 24

Orpha code: 444458OMIM code: 616239

Definition

Combined oxidative phosphorylation defect type 24 is a rare mitochondrial oxidative phosphorylation disorder characterized by variable phenotype, including developmental delay with psychomotor regression, intellectual disability, epilepsy, Leigh syndrome, non-syndromic hearing loss, visual impairment and severe myopathy. Decreased activity of mitochondrial respiratory complexes and lactic acidosis are common findings, and diffuse cerebral atrophy may be associated.

Disease data
Classification

Disease

Synonyms
COXPD24
COXPD24
ORPHA code
444458
OMIM code
616239
ICD10 code
E88.8
ICD11 code
-

No additional description.

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