Systemic polyarteritis nodosa

Orpha code: 439762OMIM code:

Definition

Systemic polyarteritis nodosa (PAN; see this term) is a chronic systemic necrotizingvasculitis of adults and childrenaffecting small- and medium-sized vessels and characterized by formation of microaneurysms leading to serious generalized disease and multi-organ involvement.

Disease data
Classification

Clinical subtype

Synonyms
Systemic PAN
Układowe PAN
Systemic periarteritis nodosa
ORPHA code
439762
OMIM code
-
ICD10 code
M30.0
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl