Colobomatous optic disc-macular atrophy-chorioretinopathy syndrome

Orpha code: 435930OMIM code: 212550

Definition

A rare genetic eye disease characterized by optic disc anomalies (bilateral colobomatous optic discs, retinal vessels arising from the peripheral optic disc) and macular atrophy. Peripapillary chorioretinal atrophy and chorioretinal and iris coloboma have also been described. Patients present with horizontal nystagmus and poor visual acuity.

Disease data
Classification

Disease

ORPHA code
435930
OMIM code
212550
ICD10 code
Q14.8
ICD11 code
-

No additional description.

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