Anterior urethral valve

Orpha code: 435372OMIM code:

Definition

A rare, congenital, fetal lower urinary tract obstruction (LUTO) anomaly occurring in males and characterized by a posteriorly directed semilunar fold arising from the floor of the anterior urethra and causing urethral obstruction during micturition. The valves may be located anywhere distal to the membranous urethra. Clinical presentation is highly variable, depending on age and degree of urinary obstruction, and includes urinary incontinence, urinary retention, weak urinary stream, post-micturitional dribbling, bulging on the ventral penis, urinary tract infection, and urosepsis.

Disease data
Classification

Morphological anomaly

ORPHA code
435372
OMIM code
-
ICD10 code
Q64.7
ICD11 code
-

No additional description.

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