Adenocarcinoma of the liver and intrahepatic biliary tract

Orpha code: 424943OMIM code:

Definition

A very rare hepatic and biliary tract tumor characterized by a growth pattern ressembling that found in hepatocellular carcinomas and cholangiocarcinomas but presenting atypical histological and immunohistochemical features (such as trabecular, organoid, microcystic and/or blastemal-like architecture and inhibin A, cytokeratin 7 and/or cytokeratin 19 positivity) that do not allow a formal diagnosis of the more common aforementioned liver cancers. Patients may present abdominal distension and pain, a palpable abdominal mass and elevated liver enzymes.

Disease data
Classification

Disease

Synonyms
Adenocarcinoma of the liver and IBT
Gruczolakorak wątroby i IBT
ORPHA code
424943
OMIM code
-
ICD10 code
C22.0
ICD11 code
-

No additional description.

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