Solid pseudopapillary carcinoma of pancreas

Orpha code: 424065OMIM code:

Definition

A rare carcinoma of the pancreas characterized by a variable combination of nonspecific signs and symptoms, such as abdominal pain, jaundice, abdominal fullness, anorexia, nausea, vomiting, and weight loss. One-third of the patients are asymptomatic. The tumor has low malignant potential, but can invade locally.

Disease data
Classification

Disease

Synonyms
Pancreatic solid pseudopapillary carcinoma
Solid pseudopapillary neoplasm of the pancreas
Pancreatic solid pseudopapillary carcinoma
Solid pseudopapillary neoplasm of the pancreas
ORPHA code
424065
OMIM code
-
ICD10 code
C25.8
ICD11 code
-

No additional description.

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