Intraductal papillary mucinous carcinoma of pancreas

Orpha code: 424058OMIM code:

Definition

Intraductal papillary mucinous carcinoma of pancreas is a rare epithelial tumor of pancreas characterized by malignant, mucin-producing cystic mass, originating from the pancreatic ductal system, associated with local invasion and metastatic spread, composed of mucin-producing, columnar epithelial cells covering the dilated pancreatic ducts with a papillary structure. The presenting symptoms are non-specific and include abdominal pain, pancreatitis, steatorrhea, jaundice and diabetes. Many patients are asymptomatic at the time of diagnosis.

Disease data
Classification

Disease

Synonyms
IPMN
Pancreatic intraductal papillary mucinous carcinoma
IPMN
Pancreatic intraductal papillary mucinous carcinoma
ORPHA code
424058
OMIM code
-
ICD10 code
C25.3
ICD11 code
-

No additional description.

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