Intraductal papillary mucinous carcinoma of pancreas

Orpha code: 424058OMIM code:

Definicja

Intraductal papillary mucinous carcinoma of pancreas is a rare epithelial tumor of pancreas characterized by malignant, mucin-producing cystic mass, originating from the pancreatic ductal system, associated with local invasion and metastatic spread, composed of mucin-producing, columnar epithelial cells covering the dilated pancreatic ducts with a papillary structure. The presenting symptoms are non-specific and include abdominal pain, pancreatitis, steatorrhea, jaundice and diabetes. Many patients are asymptomatic at the time of diagnosis.

Disease data
Klasyfikacja

Disease

Synonimy
IPMN
Pancreatic intraductal papillary mucinous carcinoma
IPMN
Pancreatic intraductal papillary mucinous carcinoma
Kod ORPHA
424058
Kod OMIM
-
Kod ICD10
C25.3
Kod ICD11
-

No additional description.

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